儿童Ph_急性淋巴细胞白血病研究进展.pdf
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2008 6 23 6 465
: 1005- 2224( 2008) 06- 0465- 03
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Ph
郭 晔 综述, 竺晓凡 审校
: R 2 : A
Ph染色体阳性; 急性淋巴细胞白血病; 研究进展
K eyw ord s Ph chromosom e pos itive; Acute lymphoblastic leukem ia; Research progress
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(ALL) ALL Ph ALL B ALL,
, ALL, ,
( DFS) 80% , ALL G Ph
, Ph( Ph+ ,
ALL) ,
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, Ph ALL G, FISH
, BCR /ABL , RTPCR BCR /ABL
+
1 Ph ALL
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1. 1 Ph ALL Ph 2 Ph ALL
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Now ell 1960, 2. 1 Ph ALL 2/3
+ [ 1]
Ph ALL, H eerem a
, bcr/abl, 3: 1
, P210P190P230P210 P ( ) 9P( 50
( CML) 50% ALL + Ph); 2 + Ph
ALL, P190 50% ALL 90% () 50 ( );
ALL, P230, 3,
, , +
Ph ALL ,
,
, +
2. 2 Ph ALL
[ 1]
H eerema BFMPOGSJCRH 10
( ) 1986 1996 326
bcr/abl bcr,
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